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The Respiratory Management of Patients With Duchenne Muscular Dystrophy: A DMD Care Considerations Working Group Specialty Article

Lookup NU author(s): Emerita Professor Katherine Bushby, Dr Michelle Eagle


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In 2001, the Muscular Dystrophy Community Assistance, Research and Education Amendments (MD-CARE Act) was enacted, which directed federal agencies to coordinate the development of treatments and cures for muscular dystrophy. As part of the mandate, the Centers for Disease Control and Prevention (CDC) initiated surveillance and educational activities, which included supporting development of care considerations for Duchenne muscular dystrophy (DMD) utilizing the RAND/UCLA Appropriateness Method (RAM). This document represents the consensus recommendations of the project's 10-member Respiratory Panel and includes advice on necessary equipment, procedures and diagnostics; and a structured approach to the assessment and management of the respiratory complications of DMD via assessment of symptoms of hypoventilation and identification of specific thresholds of forced vital capacity, peak cough flow and maximum expiratory pressure. The document includes a set of Figures adaptable as "pocket guides" to aid clinicians. This article is an expansion of the respiratory component of the multi-specialty article originally appearing in Lancet Neurology, comprising respiratory recommendations from the CDC Care Considerations project. Pediatr Pulmonol. 2010; 45:739-748. (C) 2010 Wiley-Liss, Inc.

Publication metadata

Author(s): Birnkrant DJ, Bushby KMD, Amin RS, Bach JR, Benditt JO, Eagle M, Finder JD, Kalra MS, Kissel JT, Koumbourlis AC, Kravitz RM

Publication type: Article

Publication status: Published

Journal: Pediatric Pulmonology

Year: 2010

Volume: 45

Issue: 8

Pages: 739-748

Print publication date: 01/08/2010

ISSN (print): 8755-6863

ISSN (electronic): 1099-0496

Publisher: John Wiley & Sons


DOI: 10.1002/ppul.21254


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